TYR EASY Tablets - ACCEPTABILITY AND TOLERANCE

  • Research type

    Research Study

  • Full title

    TYR EASY Tablets - ACCEPTABILITY AND TOLERANCE

  • IRAS ID

    272118

  • Contact name

    Anita MacDonald

  • Contact email

    anita.macdonald@nhs.net

  • Sponsor organisation

    Galen Ltd

  • Duration of Study in the UK

    0 years, 3 months, 25 days

  • Research summary

    Summary of Research

    The principle treatment for children with Tyrosinaemia (TYR) is a low protein diet. Part of this treatment requires the administration of a protein substitute. Several brands of protein substitutes are already available in the UK in various
    presentations. However, compliance with taking protein substitutes continues to be a challenge. As a low protein diet is recommended for life, long term compliance is a growing concern. As a result, improving the choice in terms of product type may aid compliance.
    This is a prospective, observational market research study in 8 children with TYR to evaluate the acceptability, tolerance and compliance with TYR EASY Tablets, a protein substitute for use in the dietary management of patients with TYR from 8 years and above.
    Subjects who are currently taking a protein substitute for TYR will be recruited for a 28-day trial of the new protein substitute to evaluate the tolerability and acceptability of the study product.
    During the 28-day trial patients or caregivers(depending on ability) will be asked to complete a daily questionnaire recording information on:
    • Usage and compliance
    • Ease of use and any issues with administration
    • Any gastro-intestinal side-effects
    A questionnaire will also be completed at the beginning and end of the study that will consider perceptions about taste, appearance, smell, presentation and packaging of the product; ease of administration; how it is taken; and any other problems or symptoms.
    The outcome of this assessment will be used in a submission to regulatory authorities to get the study product reimbursable on prescription in the UK.

    Summary of Results

    This is the first tablet to be used as a protein substitute in tyrosinemia. Despite the large number of tablets that need to be taken each day the subject group who took the tablets overwhelmingly preferred them to a liquid or spoonable protein substitute. In the 5 children who completed the 28 day study, all of them had improved metabolic control with 100% (n=5) having a lower tyrosine concentration. When compared with the previous 12 months 60% (n=3) compared to 20% (n=1) met the recommended target tyrosine concentrations (200-400μmol/L).

  • REC name

    HSC REC B

  • REC reference

    19/NI/0219

  • Date of REC Opinion

    8 Jan 2020

  • REC opinion

    Further Information Favourable Opinion