The Genetics of Cholesteatoma

  • Research type

    Research Study

  • Full title

    An Analysis of the Pedigrees and Genetic Profile of Patients and Families of Patients with Cholesteatoma

  • IRAS ID

    186786

  • Contact name

    Peter Prinsley

  • Contact email

    prinsley@mac.com

  • Sponsor organisation

    University of East Anglia

  • Duration of Study in the UK

    1 years, 11 months, 27 days

  • Research summary

    A clinical observation that a form of ear disease called cholesteatoma appears to run in families has been made in East Anglia. Cholesteatoma is chronic and potentially serious cause of deafness where there is destruction of the delicate structures of the ear and is treated by ear surgery. We are seeking to identify family pedigrees and subsequently to collect blood samples for genetic analysis. The aim of this study is to identify a genetic basis for the disease. We will identify families from clinical records and through the network of the British Society of Otology. We will approach these families to ask for their consent to provide family trees and subsequently blood samples. The latter will be used for a form of analysis known as genome sequencing which will provide information on any any significant variants that are associated with the clinical trait.

  • REC name

    East of England - Cambridge Central Research Ethics Committee

  • REC reference

    16/EE/0131

  • Date of REC Opinion

    22 Jun 2016

  • REC opinion

    Further Information Favourable Opinion