TEMPEST

  • Research type

    Research Study

  • Full title

    A randomised, double-blind, placebo-controlled, phase 2 evaluation of the efficacy and mechanism of trientine in patients with hypertrophic cardiomyopathy.

  • IRAS ID

    283265

  • Contact name

    Christopher Miller

  • Contact email

    christopher.miller@manchester.ac.uk

  • Sponsor organisation

    Manchester University NHS Foundation Trust

  • Eudract number

    2020-002242-17

  • Clinicaltrials.gov Identifier

    NCT04706429

  • Duration of Study in the UK

    3 years, 0 months, 1 days

  • Research summary

    Hypertrophic cardiomyopathy (HCM) is the most common inherited heart condition. It leads to abnormal thickening and scarring of the walls of the heart. As a result, the heart can have trouble pumping blood as well as it should. This causes patients to develop breathing difficulties, chest pain and fainting, which often get worse with exercise, and therefore can limit physical activity. Current treatments only aim to relieve the symptoms. There are no treatments that correct the underlying damage to the heart. Patients, caregivers and researchers have identified a “critical need” for trials of medicines that target the HCM disease process.

    Several studies in other diseases have shown that copper imbalance is associated with heart thickening similar to HCM, and that treatment with trientine, an oral medicine that increases copper removal in urine, can reverse this thickening.

    This study will investigate whether trientine reduces heart muscle thickening, improves exercise capacity, improves heart function and reduces abnormal heart rhythms in patients with HCM. The study will also assess how trientine works in HCM.

    This research study aims to recruit 172 patients with HCM aged 18-70 years in the UK. Participants in the study will be prescribed either trientine or placebo for 1 year to compare the difference.

  • REC name

    North West - Greater Manchester South Research Ethics Committee

  • REC reference

    20/NW/0275

  • Date of REC Opinion

    21 Jul 2020

  • REC opinion

    Further Information Favourable Opinion