PROMWiSe V0.2

  • Research type

    Research Study

  • Full title

    Measuring What Matters in Wolfram Syndrome: A group concept mapping exercise to facilitate identification of the most appropriate PROMs for use in clinical trials and practice for children and adults living with Wolfram Syndrome.

  • IRAS ID

    238627

  • Contact name

    Anita Slade

  • Contact email

    a.l.slade@bham.ac.uk

  • Sponsor organisation

    University of Birmingham

  • Clinicaltrials.gov Identifier

    ERN_18-1380, Ethics Number

  • Duration of Study in the UK

    0 years, 5 months, 30 days

  • Research summary

    Background: Wolfram Syndrome (WS) is a rare progressive genetic disease that effects children from an early age and often results in premature death from neurological complications in young adulthood. People with the syndrome have a range of issues including diabetes, visual impairment, neurological impairment and psychological issues related to the condition such as depression. As part of a larger clinical trial we wish to identify a range of patient reported outcome measures (PROMs) which are age appropriate for the issues that people living with WS identify as problematic. This will allow us to measure the impact of therapeutic interventions aimed at slowing down or improving the progression of WS, and the extent to which interventions improve patients quality of life. However, because its a rare condition we don't know which PROMS would be best to use and which issues are important to people living with Wolfram syndrome. Previous patient partner involvement (PPI) work with adults, children and their parents suggested that there were a diverse range of issues that needed to be addressed and not all of the reviewed PROMs addressed all of their issues. Therefore, we want to do a group concept mapping exercise with children, young adults and and adults living with Wolfram syndrome to identify which symptoms have the most impact on their life. This will allow us to identify the most suitable and age appropriate PROMs to measure changes in their symptoms and the impact on their quality of life.

  • REC name

    West Midlands - South Birmingham Research Ethics Committee

  • REC reference

    19/WM/0220

  • Date of REC Opinion

    19 Aug 2019

  • REC opinion

    Further Information Favourable Opinion