POLARIS

  • Research type

    Research Study

  • Full title

    An Observational Study in Subjects to Follow the Progression of Stargardt Disease Type 1 (STGD1) Caused by Bi-Allelic Autosomal Recessive Mutations in the ATP Binding Cassette Subfamily A Member 4 (ABCA4) Gene (POLARIS)

  • IRAS ID

    339659

  • Contact name

    Mariya Moosajee

  • Contact email

    m.moosajee@nhs.net

  • Sponsor organisation

    Splice Bio SL

  • Duration of Study in the UK

    3 years, 9 months, 23 days

  • Research summary

    Stargardt Disease Type 1 (STGD1) is a rare, progressive disease which leads to visual impairment and central vision loss. STGD1 generally occurs in childhood or adolescence but can occur into adulthood. Currently there are no approved treatments or cure for STGD1.

    This is an observational study, funded by Splice Bio, monitoring the progression of STGD1. The purpose of this study is to observe and gather information from patients with STGD1 to identify the common signs and symptoms of the disease which will then aid in the future development of treatments.

    Approximately 75 participants, aged 12 to 65, will be enrolled in this study across 20 centres globally. The study will consist of a screening phase (to ensure participants meet all eligibility criteria to take part in the study) and an observational phase and will run for up to 96 weeks for each participant.

    The primary study objective is to evaluate disease progression through various eye examinations and questionnaires.

  • REC name

    East Midlands - Nottingham 2 Research Ethics Committee

  • REC reference

    24/EM/0075

  • Date of REC Opinion

    29 Apr 2024

  • REC opinion

    Further Information Favourable Opinion