Phenotyping and Genotyping in HAE-nC1

  • Research type

    Research Study

  • Full title

    Phenotyping and Genotyping in HAE-nC1

  • IRAS ID

    369920

  • Contact name

    Nishantha Padmalal Gurugama

  • Contact email

    Padmalal.Gurugama@nhs.net

  • Sponsor organisation

    Cambridge University Hospitals NHS Foundation Trust

  • Duration of Study in the UK

    5 years, 0 months, 1 days

  • Research summary

    In this study we are looking to better understand which gene mutations cause HAE-nC1. We will do this by undertaking gene testing in a cohort of patients with features of bradykinin-mediated angioedema. This means we are trying to understand how changes in DNA (genes) result in angioedema that can be passed down from parents to children, in a group of people with normal levels and functions of C1-esterase inhibitor protein.

    We will do this by collecting clinical information, assessing biomarkers (C4, C3, C1 level and function, bradykinin levels and their breakdown products) and genetic screening.

  • REC name

    West of Scotland REC 5

  • REC reference

    26/WS/0046

  • Date of REC Opinion

    28 May 2026

  • REC opinion

    Further Information Favourable Opinion