LSEP Study

  • Research type

    Research Study

  • Full title

    AN OPEN-LABEL, SAFETY STUDY FOR PREVIOUSLY TREATED VATIQUINONE (PTC743) SUBJECTS WITH INHERITED MITOCHONDRIAL DISEASE

  • IRAS ID

    1006123

  • Contact name

    Vinay Penematsa

  • Contact email

    medinfo@ptcbio.com

  • Sponsor organisation

    PTC THERAPEUTICS, INC.

  • Eudract number

    2022-000375-39

  • Clinicaltrials.gov Identifier

    NCT04378075

  • Research summary

    This is an open-label, Phase 3 safety study of vatiquinone in subjects with inherited mitochondrial disease who were previously treated with vatiquinone at an investigational site in a prior PTC/BioElectron-sponsored clinical study or treatment plan (parent study). A target of approximately 200 previously treated vatiquinone subjects will be enrolled at up to approximately 40 investigational sites worldwide.
    Participants: Subjects with inherited mitochondrial disease including Leigh syndrome, Alpers Syndrome, mitochondrial encephalomyopathy, lactic acidosis and stroke-like episodes (MELAS), myoclonic epilepsy with ragged-red fibers (MERRF), pontocerebellar hypoplasia type 6 (PCH6), or other mitochondrial disease who participated in a previous vatiquinone clinical study or treatment plan.
    Subjects will receive vatiquinone oral solution (100 mg/mL), up to 400 mg, administered orally or via feeding tube TID. Subjects will continue the dosing regimen from their parent study.
    Safety assessments for subjects will be performed at screening/baseline and every 6 months until vatiquinone becomes commercially available or the program is terminated. Safety assessments will also be collected for all subjects at the End-of-Treatment Visit.

    Primary objective: to assess the safety of vatiquinone in subjects with inherited mitochondrial disease who had prior exposure to vatiquinone in a PTC/BioElectron-sponsored (previously Edison) clinical study or treatment plan.
    Exploratory: to explore the effects of vatiquinone in total seizure count in subjects previously enrolled in vatiquinone Study MIT-E.
    Sponsor: PTC Therapeutics.

  • REC name

    Wales REC 3

  • REC reference

    22/WA/0290

  • Date of REC Opinion

    5 Dec 2022

  • REC opinion

    Further Information Favourable Opinion