Long Term Extension Study of A4250 in Children with PFIC (PEDFIC 2)

  • Research type

    Research Study

  • Full title

    An Open-label Extension Study to Evaluate Long-term Efficacy and Safety of A4250 in Children with Progressive Familial Intrahepatic Cholestasis Types 1 and 2 (PEDFIC 2)

  • IRAS ID

    237500

  • Contact name

    Tassos Grammatikopoulos

  • Contact email

    t.grammatikopoulos@nhs.net

  • Sponsor organisation

    Ipsen Pharma

  • Eudract number

    2017-002325-38

  • Clinicaltrials.gov Identifier

    NCT03566238

  • Duration of Study in the UK

    2 years, 4 months, 1 days

  • Research summary

    Progressive Familial Intrahepatic Cholestasis (PFIC) is a chronic liver disease with impaired bile flow and patients’ also experience a severe itch. PFIC exists worldwide and both girls and boys are equally affected.
    Approximately half of PFIC patients undergo liver transplants. Many patients also undergo Partial External Biliary Diversion, which is a surgery to divert/drain bile away form the liver to try and improve persistent, treatment resistant
    itching.
    Currently, the treatment is palliative and there is no medical treatment approved for use in PFIC.
    A4250 is a research medicine that is being developed to treat patients with PFIC. A4250 is believed to reduce the absorption of bile acids from the intestine and lower bile acid levels in the blood. A4250 has so far been tested on
    healthy volunteers and in a study in children with any of several cholestatic (impaired bile flow) liver diseases, including some with PFIC.
    This is a Phase 3, multi-centre, open-label extension study to investigate the long-term effectiveness and safety of a 120 microgramme daily dose of A4250 in children with PFIC Types 1 and 2 who have completed Study A4250-005: A Double-Blind, Randomized, Placebo-Controlled, Phase 3 Study to Demonstrate Efficacy and Safety of A4250 in Children with Progressive Familial Intrahepatic Cholestasis Types 1 and 2 (PEDFIC 1).
    There are 2 stages to this study: Treatment Period and Follow Up. Approximately 60 participants will take part in the study at about 50 clinics in 15 countries.The study will last for approx 18 months.
    Participants will need to have a number of different tests to determine if the study drug works and what side effects there might be, including: physical examinations, blood and urine tests, ultrasounds and vital sign checks.

  • REC name

    London - Dulwich Research Ethics Committee

  • REC reference

    18/LO/1585

  • Date of REC Opinion

    2 Nov 2018

  • REC opinion

    Further Information Favourable Opinion