LCU-ALS NREScommittee london bloomsburry 15/LO/0059

  • Research type

    Research Study

  • Full title

    Genetic post-hoc analysis of blind randomised controlled trials of Lithium Carbonate in patients with Amyotrophic Lateral Sclerosis. Is Lithium Carbonate beneficial to homozygous UNC13a ALS patients?

  • IRAS ID

    168859

  • Contact name

    Ammar / A. Al-Chalabi

  • Contact email

    ammar.al-chalabi@kcl.ac.uk

  • Sponsor organisation

    King’s College London

  • Duration of Study in the UK

    0 years, 3 months, 0 days

  • Research summary

    Amyotrophic lateral sclerosis (ALS) is a devastating, fatal neurologic disease for which there is no effective treatment. Based on promising results in animal studies several trials with lithium in ALS were performed, but were unfortunately all negative. Recent research has shown that certain genetic variants (UNC13a and C9orf72) negatively influence survival in ALS and may thus also effect the outcome of clinical trials. Longstanding collaborators in The Netherlands have reanalyzed their lithium trial taking these genetic variants into account and their data suggests that lithium may be beneficial to patients with UNC13a variants. ALS patients with UNC13a variants treated with lithium had a mean survival of 16.9 months (SE 3.3) compared to 9.5 months (SE 1.5) for ALS patients with UNC13a variants treated with placebo. Although the Dutch data is very promising, the number of UNC13a ALS patients was relatively small and therefore a definitive conclusion could not be reached. Therefore we propose to perform a genetic post-hoc analysis on 3 lithium trials in ALS conducted in The Netherlands (LITRA), Italy (LITALS) and the UK (LiCALS).
    In the UK the majority of ALS patients donate DNA samples to the MND DNA bank. These samples have all been analyzed for variants in many genes, including UNC13a and C9orf72 (prof Al-Chalabi is also chief investigator on the genetic studies). Therefore, genetic data will likely be available for the participants of the LiCALS trial. The main purpose for this application is to request permission to temporarily reverse the anonymisation in the LiCALS trial, so the genetic data can be linked to the trial data to facilitate this genetic post-hoc analysis.
    The possibility that lithium could be effective in a specific group of ALS patients is very exciting and could be a huge, much needed step forward in the treatment of this detrimental disease.

  • REC name

    London - Bloomsbury Research Ethics Committee

  • REC reference

    15/LO/0059

  • Date of REC Opinion

    11 Feb 2015

  • REC opinion

    Favourable Opinion