Exome Sequencing to Determine Causative Genes in Knee Joint Dysplasia

  • Research type

    Research Study

  • Full title

    Use of Whole Exome Sequencing to Determine Causative Genes in a Single Pedigree with Femoral Trochlear Dysplasia.

  • IRAS ID

    165628

  • Contact name

    Karen Shepherd

  • Contact email

    karen.shepherd@nnuh.nhs.uk

  • Sponsor organisation

    Norfolk and Norwich University Hospitals NHS Foundation Trust

  • Duration of Study in the UK

    0 years, 3 months, 0 days

  • Research summary

    The underlying cause of dysplastic (abnormally structured) joints remains poorly understood. Previous studies have shown a strong pattern of inheritance of joint dysplasia, suggesting a genetic component to its aetiology. Exome sequencing is a new method for identifying causative genes of rare inherited conditions that involves sequencing all of the protein­ coding DNA of an individual and identifying abnormal genes by reference to known databases. We have identified a family demonstrating a clear pattern of inheritance of knee joint dysplasia and aim to use Exome sequencing in addition to traditional sequencing methods to identify novel causative genes. Identification of genes associated with joint dysplasia could lead to earlier diagnosis and therefore more successful interventions.

  • REC name

    East of England - Essex Research Ethics Committee

  • REC reference

    15/EE/0009

  • Date of REC Opinion

    24 Feb 2015

  • REC opinion

    Further Information Favourable Opinion