Exercise and Neurodegeneration Related to G4C2 Expansion of C9ORF72

  • Research type

    Research Study

  • Full title

    The Role of Exercise in Modifying Neurodegeneration Related to G4C2 Repeat Expansion of C9ORF72.

  • IRAS ID

    189432

  • Contact name

    Johnathan Cooper-Knock

  • Contact email

    j.cooper-knock@sheffield.ac.uk

  • Sponsor organisation

    Sheffield Teaching Hospitals NHS Foundation Trust

  • Duration of Study in the UK

    0 years, 11 months, 26 days

  • Research summary

    Motor neurone disease (MND) is a severe condition caused by damage to the nervous system. MND often progresses rapidly, resulting in weakness of the limbs and difficulty with speech, swallowing and breathing. Unfortunately, at present, there are few effective treatments for MND and patients usually die within 3 years of onset. The causes of MND are unknown; however, people with certain gene mutations are more likely to be affected by this fatal condition. The most common abnormality found in patients with MND is an increased number of G4C2 repeats in the C9ORF72 gene.
    It has been proposed that physical activity (PA) increases the risk of MND. However, studies so far have been inconclusive. It is for this reason that we aim to undertake a study investigating previous levels of PA in people with the C9ORF72 mutation, both with MND and healthy volunteers. Over one year, we will recruit approximately 30 patients newly diagnosed with MND who are known to have the C9ORF72 mutation. We will conduct interviews with each patient using a questionnaire which measures PA throughout a person’s adult life. We will compare this with information previously collected from healthy volunteers who also share the C9ORF72 mutation but do not have MND.
    We propose that the mutation in the C9ORF72 gene in combination with participation in a high level of PA is associated with an increased risk of MND. As a result, we hope to gain greater insight into a condition that remains ambiguous. Ultimately, by increasing our understanding of MND, this will hopefully contribute to the development of new treatments for a currently fatal condition.

  • REC name

    North West - Liverpool Central Research Ethics Committee

  • REC reference

    15/NW/0836

  • Date of REC Opinion

    26 Oct 2015

  • REC opinion

    Further Information Favourable Opinion