Drisapersen extension study

  • Research type

    Research Study

  • Full title

    An open-label extension study of the long-term safety, tolerability and efficacy of drisapersen in subjects with Duchenne Muscular Dystrophy.

  • IRAS ID

    189216

  • Contact name

    Francesco Muntoni

  • Contact email

    f.muntoni@ucl.ac.uk

  • Sponsor organisation

    BioMarin Pharmaceutical Inc.

  • Eudract number

    2015-001955-54

  • Duration of Study in the UK

    1 years, 11 months, 30 days

  • Research summary

    Duchennes Muscular Dystrophy (DMD) is a genetically inherited disease linked to the X chromosome and affects approximately 1 in 3500 newborn boys. DMD is Life Limiting and due to it's symptoms being delayed motor milestones and being able to run and jump properly, most are diagnosed at about age 5. If left untreated, most boys will require the use of a wheelchair before their teens.

    The purpose of this study is to provide re-access to drisapersen for patients who previoulsy participated in drisapersen studies and cannot take part in ongoing studies. Participants will be provided drisapersen until it is commercially available in their country.
    Participants will receive drisapersen administered either as continuous 6mg/kg/week via subcutaneous injection, intermittent 6mg/kg/week for 8 weeks followed by 4 weeks no dosing or intravenous infusion of a maximum 6mg/kg/week over a 2 hour infusion.
    The duration of participation will cary dependant upon, regulatory approval/refusal, patients having serious adverse events and having to withdraw from the study or if the sponsor withdraws due to safety and efficacy findings.

    Study sites: this study is to be conducted at approximately 90 sites worldwide.

  • REC name

    London - Riverside Research Ethics Committee

  • REC reference

    15/LO/1657

  • Date of REC Opinion

    26 Nov 2015

  • REC opinion

    Further Information Favourable Opinion