Developing Classification Criteria for Juvenile Systemic Sclerosis

  • Research type

    Research Study

  • Full title

    Developing Classification Criteria for Juvenile Systemic Sclerosis

  • IRAS ID

    332344

  • Contact name

    Clare Pain

  • Contact email

    clare.pain@alderhey.nhs.uk

  • Sponsor organisation

    Alder Hey Children's Hospital NHS Foundation Trust

  • Clinicaltrials.gov Identifier

    N/A, N/A

  • Duration of Study in the UK

    2 years, 11 months, 30 days

  • Research summary

    Systemic sclerosis is an autoimmune condition that causes inflammation, changes in blood vessels, and thickening and scarring of various organs, including the skin, heart, lungs, kidneys and gastrointestinal tract. Juvenile systemic sclerosis (jSSc) affects children and is associated with high morbidity and a significant risk of mortality. This condition is rare and can be challenging to identify, resulting in limited studies done on jSSc. Current treatment plans for affected children are derived from studies conducted in adults.

    Adult systemic sclerosis and jSSc have different disease patterns and therefore current treatment plans for children may not be the most appropriate. This study will aim to develop a classification criterion for jSSc. This classification criteria will help researchers worldwide conduct studies on jSSc which will then lead to an increase in our understanding of the condition and how best to treat it. The information gathered during this study can also be used by doctors and healthcare professionals to help diagnose jSSc in children and it can measure how well current medications improve symptoms.

    To create this classification tool, we will gather data from participant medical records. This will include information from children with jSSc as well as children who have been diagnosed with conditions similar to jSSc (referred to as jSSc mimickers in this study). This comprehensive dataset will allow us to distinguish more effectively between the features of jSSc and its mimickers, and therefore develop a set of criteria that are more accurate for identifying jSSc in children.

  • REC name

    West Midlands - Coventry & Warwickshire Research Ethics Committee

  • REC reference

    24/WM/0180

  • Date of REC Opinion

    13 Aug 2024

  • REC opinion

    Favourable Opinion