Dental health in rare genetic conditions v1.0

  • Research type

    Research Study

  • Full title

    An outpatient study of dental health in children with rare genetic conditions

  • IRAS ID

    347722

  • Contact name

    Alisdair McNeill

  • Contact email

    a.mcneill@sheffield.ac.uk

  • Sponsor organisation

    the University of Sheffield

  • Duration of Study in the UK

    5 years, 0 months, 1 days

  • Research summary

    In this project, we will characterise the dental health of children with recently discovered genetic causes of intellectual disability (ID). Large scale genomic sequencing projects, such as Deciphering Developmental Disorders (DDD), SOLVE-RD and the 100 000 genomes project, have identified dozens of novel genetic causes of ID. Very little is known about the symptoms and health effects of these. There is an urgent clinical need to define the dental manifestations of these new genetic causes of ID. The proposed research will use a calibrated dental examination to define dental manifestations in children affected by the top 10 genomic conditions diagnosed in large scale UK genome sequencing projects. This will identify the prevalence of dental malformations in these individuals and also characterise general dental health. This will inform the clinical practice of Paediatricians and Paediatric dental teams.

  • REC name

    North West - Haydock Research Ethics Committee

  • REC reference

    24/NW/0344

  • Date of REC Opinion

    4 Nov 2024

  • REC opinion

    Favourable Opinion