Characterising electrophysiological patterns in neuromuscular disease

  • Research type

    Research Study

  • Full title

    Characterising electrophysiological patterns in neuromuscular disease over time using serial neurophysiology studies

  • IRAS ID

    193889

  • Contact name

    Stephanie Blacklock

  • Contact email

    stephanie.blacklock@nuth.nhs.uk

  • Sponsor organisation

    The Newcastle Upon Tyne Hospitals NHS Foundation Trust

  • Duration of Study in the UK

    1 years, 5 months, 31 days

  • Research summary

    Many patients with rare neuromuscular diseases have a failure of neurotransmission, or the ability of nerves to conduct impulses to muscles. Little is known about how this failure of neurotransmission changes over disease course, or how it is affected by current available treatments. In this study we will perform serial neurophysiological studies in volunteers with neuromuscular disorders, in order to assess how neurotransmission changes during disease course and with treatment. Research participants will have neurophysiology studies carried out after their assessment at the specialist neuromuscular clinic in Newcastle on 3 occasions 6 months apart. To support the information from the neurophysiology tests, researchers will also record the clinical information recorded at the participants clinic attendance (information on symptoms and muscle strength). The combined results from these patients will be used to provide new information on the mode of action of the standard treatments currently given to these patients, and this information will contribute towards the development of new more targeted therapies. In addition, the research will provide important information relating to disease course which can be used in providing end-points for future clinical trials.

  • REC name

    North East - Newcastle & North Tyneside 1 Research Ethics Committee

  • REC reference

    16/NE/0161

  • Date of REC Opinion

    4 Aug 2016

  • REC opinion

    Further Information Favourable Opinion