* APPOINT-PNH

  • Research type

    Research Study

  • Full title

    A multicenter, single-arm, open-label trial to evaluate efficacy and safety of oral, twice daily iptacopan in adult PNH patients who are naive to complement inhibitor therapy

  • IRAS ID

    293217

  • Contact name

    Austin Kulasekararaj

  • Contact email

    austin.kulasekararaj@nhs.net

  • Sponsor organisation

    Novartis Pharma AG

  • Eudract number

    2020-003172-41

  • Clinicaltrials.gov Identifier

    NCT04820530

  • Clinicaltrials.gov Identifier

    N/A, N/A

  • Duration of Study in the UK

    1 years, 10 months, 4 days

  • Research summary

    Research Summary: This is a multicentre, single arm, phase 3, open-label trial which aims to determine whether iptacopan is efficacious and safe for the treatment of Paroxysmal Nocturnal Haemoglobinuria (PNH) in patients who have not previously been treated with the standard of care anti-C5 antibody therapies. PNH is a rare disease which causes haemolysis of red blood cells, releasing haemoglobin, which leads to, amongst other symptoms, severe anaemia. The study will treat 40 adult patients (male and female) and the patients will participate in an 8 week screening period, a 24 week core treatment period and a 24 extension treatment period. The aim of the study is to assess whether treatment with iptacopan will achieve a sustained increase in the patients' haemoglobin levels by ≥ 2g/dL. This measurement confirms patients are not affected by haemolysis. In addition clinical assessments will also measure whether patients treated with iptacopan can achieve haemoglobin levels ≥ 12 g/dL (patients would be considered no longer clinically anaemic) in the absence of red blood cell transfusions. In addition to clinical assessments, changes in patients' quality of life are assessed through patient questionnaires and, in some countries (not UK), a patient interview.

    Summary of results: This is a multicentre, single arm, phase 3, open-label trial which aims to determine whether iptacopan is efficacious and safe for the treatment of Paroxysmal Nocturnal Haemoglobinuria (PNH) in patients who have not previously been treated with the standard of care anti-C5 antibody therapies. PNH is a rare disease which causes haemolysis of red blood cells, releasing haemoglobin, which leads to, amongst other symptoms, severe anaemia. The study will treat 40 adult patients (male and female) and the patients will participate in an 8 week screening period, a 24 week core treatment period and a 24 extension treatment period. The aim of the study is to assess whether treatment with iptacopan will achieve a sustained increase in the patients' haemoglobin levels by = 2g/dL. This measurement confirms patients are not affected by haemolysis. In addition clinical assessments will also measure whether patients treated with iptacopan can achieve haemoglobin levels = 12 g/dL (patients would be considered no longer clinically anaemic) in the absence of red blood cell transfusions. In addition to clinical assessments, changes in patients' quality of life are assessed through patient questionnaires and, in some countries (not UK), a patient interview.

  • REC name

    London - Westminster Research Ethics Committee

  • REC reference

    21/FT/0071

  • Date of REC Opinion

    16 Jun 2021

  • REC opinion

    Further Information Favourable Opinion