Alkaptonuria Questionnaire Study

  • Research type

    Research Study

  • Full title

    Alkaptonuria Questionnaire study

  • IRAS ID

    242534

  • Contact name

    Lakshminarayan Ranganath

  • Contact email

    lrang@liv.ac.uk

  • Sponsor organisation

    University of Liverpool

  • Duration of Study in the UK

    2 years, 7 months, 31 days

  • Research summary

    Alkaptonuria (AKU) is a genetic disorder present from birth affecting men and women from around age 30 years. The disease manifests earlier in men compared with women. Severity of manifestations including musculoskeletal are variable and unpredictable. Since AKU is a disturbance in the tyrosine (protein) pathway, diet is expected to influence severity. Since major manifestations affect cartilage, physical activity is also expected to influence the severity. Although AKU is a monogenic disease, background osteoarthritis is family way affect severity. Collecting to event data on manifestations enables a better understanding of severity of AKU and factors affecting AKU beyond the genetic. For these reasons we propose to collect questionnaire data relating to family history of arthritis, timeline of morbid features of AKU, one year and life time dietary analysis, as well as short term (one week) and lifetime physical activity data for analysis.

  • REC name

    HSC REC B

  • REC reference

    18/NI/0086

  • Date of REC Opinion

    15 May 2018

  • REC opinion

    Further Information Favourable Opinion