A phase 1/2 study of GTX-102 in paediatric patients with AS

  • Research type

    Research Study

  • Full title

    A Phase 1/2 Open-label, Multiple-dose, Dose-escalating Clinical Trial of the Safety and Tolerability of GTX-102 in Pediatric Patients With Angelman Syndrome (AS)

  • IRAS ID

    299037

  • Contact name

    Laurent Servais

  • Contact email

    laurent.servais@paediatrics.ox.ac.uk

  • Sponsor organisation

    GeneTx Biotherapeutics, LLC

  • Eudract number

    2021-001793-36

  • Clinicaltrials.gov Identifier

    NCT04259281

  • Duration of Study in the UK

    3 years, 0 months, 1 days

  • Research summary

    Angelman Syndrome (AS) is a genetic condition that affects the nervous system and causes severe physical and learning disabilities. There are currently no approved therapies specifically indicated for the treatment of AS.

    The purpose of this study is to determine the safety and tolerability of an investigational medicine, called GTX-102, in paediatric patients with AS. The study will also assess how well GTX-102 is processed in the participants body and its effectiveness.

    The study consists of two phases: the Dose Escalation Phase and the Maintenance Phase. The Dose Escalation Phase is the initial part of the study where participants will receive GTX-102 monthly.

    Participants will be enrolled into 1 of 2 cohorts: Cohort 4 or Cohort 5, and will receive 3-4 doses of GTX-102. After completion of the Dose Escalation Phase, participants will continue into the Maintenance Phase and will receive GTX-102 approximately every 3 months.

    This is an open-label study meaning all participants will receive GTX-102.

    GeneTx Biotherapeutics, LLC is sponsoring this multicenter study, with approximately 8 to 12 study sites in the United States, United Kingdom, and Canada.

  • REC name

    South Central - Berkshire Research Ethics Committee

  • REC reference

    21/SC/0168

  • Date of REC Opinion

    24 May 2021

  • REC opinion

    Favourable Opinion